Publications of A. Wredenberg

Journal Article (8)

2020
Journal Article
Alsina, D.; Lytovchenko, O.; Schab, A.; Atanassov, I.; Schober, F. A.; Jiang, M.; Koolmeister, C.; Wedell, A.; Taylor, R. W.; Wredenberg, A. et al.; Larsson, N.G.: FBXL4 deficiency increases mitochondrial removal by autophagy. EMBO Mol Med 12 (7), p. e11659 (2020)
2019
Journal Article
Gopalakrishna, S.; Pearce, S. F.; Dinan, A. M.; Schober, F. A.; Cipullo, M.; Spahr, H.; Khawaja, A.; Maffezzini, C.; Freyer, C.; Wredenberg, A. et al.; Atanassov, I.; Firth, A. E.; Rorbach, J.: C6orf203 is an RNA-binding protein involved in mitochondrial protein synthesis. Nucleic Acids Res 47 (17), pp. 9386 - 9399 (2019)
Journal Article
Filograna, R.; Koolmeister, C.; Upadhyay, M.; Pajak, A.; Clemente, P.; Wibom, R.; Simard, M. L.; Wredenberg, A.; Freyer, C.; Stewart, J. et al.; Larsson, N.G.: Modulation of mtDNA copy number ameliorates the pathological consequences of a heteroplasmic mtDNA mutation in the mouse. Sci Adv 5 (4), p. eaav9824 (2019)
2017
Journal Article
Siibak, T.; Clemente, P.; Bratic, A.; Bruhn, H.; Kauppila, T. E. S.; Macao, B.; Schober, F. A.; Lesko, N.; Wibom, R.; Naess, K. et al.; Nennesmo, I.; Wedell, A.; Peter, B.; Freyer, C.; Falkenberg, M.; Wredenberg, A.: A multi-systemic mitochondrial disorder due to a dominant p.Y955H disease variant in DNA polymerase gamma. Hum Mol Genet 26 (13), pp. 2515 - 2525 (2017)
2015
Journal Article
Bratic, A.; Kauppila, T. E. S.; Macao , B.; Grönke, S.; Siibak, T.; Stewart, J. B.; Baggio, F.; Dols, J.; Partridge, L.; Falkenberg, M. et al.; Wredenberg, A.; Larsson, N.G.: Complementation between polymerase- and exonuclease-deficient mitochondrial DNA polymerase mutants in genomically engineered flies. Nat Commun 6, p. 8808 (2015)
2013
Journal Article
Wredenberg, A.; Lagouge, M.; Bratic, A.; Metodiev, M. D.; Spahr, H.; Mourier, A.; Freyer, C.; Ruzzenente, B.; Tain, L. S.; Grönke, S. et al.; Baggio, F.; Kukat, C.; Kremmer, E.; Wibom, R.; Polosa, P. L.; Habermann, B.H.; Partridge, L.; Park, C. B.; Larsson, N.G.: MTERF3 regulates mitochondrial ribosome biogenesis in invertebrates and mammals. PLoS Genet 9 (1), p. e1003178 (2013)
2012
Journal Article
Ruzzenente, B.; Metodiev, M. D.; Wredenberg, A.; Bratic, A.; Park, C. B.; Camara, Y.; Milenkovic, D.; Zickermann, V.; Wibom, R.; Hultenby, K. et al.; Erdjument-Bromage, H.; Tempst, P.; Brandt, U.; Stewart, J. B.; Gustafsson, C. M.; Larsson, N.G.: LRPPRC is necessary for polyadenylation and coordination of translation of mitochondrial mRNAs. EMBO J 31 (2), pp. 443 - 56 (2012)
2011
Journal Article
Bratic, A.; Wredenberg, A.; Grönke, S.; Stewart, J. B.; Mourier, A.; Ruzzenente, B.; Kukat, C.; Wibom, R.; Habermann, B.H.; Partridge, L. et al.; Larsson, N.G.: The bicoid stability factor controls polyadenylation and expression of specific mitochondrial mRNAs in Drosophila melanogaster. PLoS Genet 7 (10), p. e1002324 (2011)
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