Publications of B. Ruzzenente

Journal Article (11)

2017
Journal Article
Siira, S. J.; Spahr, H.; Shearwood, A. J.; Ruzzenente, B.; Larsson, N.G.; Rackham, O.; Filipovska, A.: LRPPRC-mediated folding of the mitochondrial transcriptome. Nat Commun 8 (1), p. 1532 (2017)
2014
Journal Article
Mourier, A.; Matic, S.; Ruzzenente, B.; Larsson, N.G.; Milenkovic, D.: The respiratory chain supercomplex organization is independent of COX7a2l isoforms. Cell Metab 20 (6), pp. 1069 - 75 (2014)
Journal Article
Kühl, I.; Kukat, C.; Ruzzenente, B.; Milenkovic, D.; Mourier, A.; Miranda, M.; Koolmeister, C.; Falkenberg, M.; Larsson, N.G.: POLRMT does not transcribe nuclear genes. Nature 514 (7521), pp. E7 - 11 (2014)
Journal Article
Metodiev , M. D.; Spahr, H.; Loguercio Polosa, P.; Meharg, C.; Becker, C.; Altmueller, J.; Habermann, B.H.; Larsson, N.G.; Ruzzenente, B.: NSUN4 is a dual function mitochondrial protein required for both methylation of 12S rRNA and coordination of mitoribosomal assembly. PLoS Genet 10 (2), p. e1004110 (2014)
Journal Article
Mourier, A.; Ruzzenente, B.; Brandt, T.; Kuhlbrandt, W.; Larsson, N.G.: Loss of LRPPRC causes ATP synthase deficiency. Hum Mol Genet 23 (10), pp. 2580 - 92 (2014)
Journal Article
Metodiev, M.D.; Spahr, H.; Polosa, P. L.; Meharg, C.; Becker, C.; Altmueller, J.; Habermann, B.H.; Larsson, N.G.; Ruzzenente, B.: NSUN4 Is a Dual Function Mitochondrial Protein Required for Both Methylation of 12S rRNA and Coordination of Mitoribosomal Assembly. PLOS GENETICS 10 (2), e1004110 (2014)
2013
Journal Article
Harmel, J.; Ruzzenente, B.; Terzioglu, M.; Spahr, H.; Falkenberg, M.; Larsson, N.G.: The leucine-rich pentatricopeptide repeat-containing protein (LRPPRC) does not activate transcription in mammalian mitochondria. J Biol Chem 288 (22), pp. 15510 - 9 (2013)
Journal Article
Milenkovic, D.; Matic, S.; Kühl, I.; Ruzzenente, B.; Freyer, C.; Jemt , E.; Park, C. B.; Falkenberg, M.; Larsson, N.G.: TWINKLE is an essential mitochondrial helicase required for synthesis of nascent D-loop strands and complete mtDNA replication. Hum Mol Genet 22 (10), pp. 1983 - 93 (2013)
2012
Journal Article
Ruzzenente, B.; Metodiev, M. D.; Wredenberg, A.; Bratic, A.; Park, C. B.; Camara, Y.; Milenkovic, D.; Zickermann, V.; Wibom, R.; Hultenby, K. et al.; Erdjument-Bromage, H.; Tempst, P.; Brandt, U.; Stewart, J. B.; Gustafsson, C. M.; Larsson, N.G.: LRPPRC is necessary for polyadenylation and coordination of translation of mitochondrial mRNAs. EMBO J 31 (2), pp. 443 - 56 (2012)
2011
Journal Article
Bratic, A.; Wredenberg, A.; Grönke, S.; Stewart, J. B.; Mourier, A.; Ruzzenente, B.; Kukat, C.; Wibom, R.; Habermann, B.H.; Partridge, L. et al.; Larsson, N.G.: The bicoid stability factor controls polyadenylation and expression of specific mitochondrial mRNAs in Drosophila melanogaster. PLoS Genet 7 (10), p. e1002324 (2011)
Journal Article
Camara, Y.; Asin-Cayuela, J.; Park, C. B.; Metodiev, M.D.; Shi, Y.; Ruzzenente, B.; Kukat, C.; Habermann, B.H.; Wibom, R.; Hultenby, K. et al.; Franz, T.; Erdjument-Bromage, H.; Tempst, P.; Hallberg, B. M.; Gustafsson, C. M.; Larsson, N.G.: MTERF4 regulates translation by targeting the methyltransferase NSUN4 to the mammalian mitochondrial ribosome. Cell Metab 13 (5), pp. 527 - 39 (2011)
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