Journal Article (1392)

1997
Journal Article
Larsson, N.G.; Oldfors, A.; Garman, J. D.; Barsh, G. S.; Clayton, D. A.: Down-regulation of mitochondrial transcription factor A during spermatogenesis in humans. Hum Mol Genet 6 (2), pp. 185 - 91 (1997)
1996
Journal Article
Langer, T.; Neupert, W.: Regulated protein degradation in mitochondria. Experientia 52 (12), pp. 1069 - 76 (1996)
Journal Article
Stuart, R. A.; Ono, H.; Langer, T.; Neupert, W.: Mechanisms of protein import into mitochondria. Cell Struct Funct 21 (5), pp. 403 - 6 (1996)
Journal Article
Schmitt, M.; Neupert, W.; Langer, T.: The molecular chaperone Hsp78 confers compartment-specific thermotolerance to mitochondria. J Cell Biol 134 (6), pp. 1375 - 86 (1996)
Journal Article
Leonhard, K.; Herrmann, J. M.; Stuart, R. A.; Mannhaupt, G.; Neupert, W.; Langer, T.: AAA proteases with catalytic sites on opposite membrane surfaces comprise a proteolytic system for the ATP-dependent degradation of inner membrane proteins in mitochondria. EMBO J 15 (16), pp. 4218 - 29 (1996)
Journal Article
Larsson, N.G.; Garman, J. D.; Oldfors, A.; Barsh, G. S.; Clayton, D. A.: A single mouse gene encodes the mitochondrial transcription factor A and a testis-specific nuclear HMG-box protein. Nat Genet 13 (3), pp. 296 - 302 (1996)
Journal Article
Arlt, H.; Tauer, R.; Feldmann, H.; Neupert, W.; Langer, T.: The YTA10-12 complex, an AAA protease with chaperone-like activity in the inner membrane of mitochondria. Cell 85 (6), pp. 875 - 85 (1996)
Journal Article
Teichmann, U.; van Dyck, L.; Guiard, B.; Fischer, H.; Glockshuber, R.; Neupert, W.; Langer, T.: Substitution of PIM1 protease in mitochondria by Escherichia coli Lon protease. J Biol Chem 271 (17), pp. 10137 - 42 (1996)
Journal Article
Langer, T.; Buchner, J.; Bukau, B.: Chaperone function on Crete: a meeting report. Cell Stress Chaperones 1 (1), pp. 5 - 12 (1996)
Journal Article
Houshmand, M.; Larsson, N.G.; Oldfors, A.; Tulinius, M.; Holme, E.: Fatal mitochondrial myopathy, lactic acidosis, and complex I deficiency associated with a heteroplasmic A --> G mutation at position 3251 in the mitochondrial tRNALeu(UUR) gne. Hum Genet 97 (3), pp. 269 - 73 (1996)
Journal Article
Prip-Buus, C.; Westerman, B.; Schmitt, M.; Langer, T.; Neupert, W.; Schwarz, E.: Role of the mitochondrial DnaJ homologue, Mdj1p, in the prevention of heat-induced protein aggregation. FEBS Lett 380 (1-2), pp. 142 - 6 (1996)
1995
Journal Article
Schmitt, M.; Neupert, W.; Langer, T.: Hsp78, a Clp homologue within mitochondria, can substitute for chaperone functions of mt-hsp70. EMBO J 14 (14), pp. 3434 - 44 (1995)
Journal Article
Oldfors, A.; Moslemi, A. R.; Fyhr, I. M.; Holme, E.; Larsson, N.G.; Lindberg, C.: Mitochondrial DNA deletions in muscle fibers in inclusion body myositis. J Neuropathol Exp Neurol 54 (4), pp. 581 - 7 (1995)
Journal Article
Holme, E.; Tulinius, M. H.; Larsson, N.G.; Oldfors, A.: Inheritance and expression of mitochondrial DNA point mutations. Biochim Biophys Acta 1271 (1), pp. 249 - 52 (1995)
Journal Article
Walum, E.; Eriksson, G.; Peterson, A.; Holme, E.; Larsson, N.G.; Eriksson, C.; el-Shamy, W.: Use of primary cultures and continuous cell lines to study effects on astrocytic regulatory functions. Clin Exp Pharmacol Physiol 22 (4), pp. 284 - 7 (1995)
Journal Article
Langer, T.; Pajic, A.; Wagner, I.; Neupert, W.: Proteolytic breakdown of membrane-associated polypeptides in mitochondria of Saccharomyces cerevisiae. Methods Enzymol 260, pp. 495 - 503 (1995)
Journal Article
Larsson, N.G.; Clayton, D. A.: Molecular genetic aspects of human mitochondrial disorders. Annu Rev Genet 29, pp. 151 - 78 (1995)
Journal Article
Larsson, N.G.; Tulinius, M. H.; Holme, E.; Oldfors, A.: Pathogenetic aspects of the A8344G mutation of mitochondrial DNA associated with MERRF syndrome and multiple symmetric lipomas. Muscle Nerve Suppl 3, pp. S102 - 6 (1995)
Journal Article
Oldfors, A.; Holme, E.; Tulinius, M.; Larsson, N.G.: Tissue distribution and disease manifestations of the tRNA(Lys) A-->G(8344) mitochondrial DNA mutation in a case of myoclonus epilepsy and ragged red fibres. Acta Neuropathol 90 (3), pp. 328 - 33 (1995)
1994
Journal Article
Wagner, I.; Arlt, H.; van Dyck, L.; Langer, T.; Neupert, W.: Molecular chaperones cooperate with PIM1 protease in the degradation of misfolded proteins in mitochondria. EMBO J 13 (21), pp. 5135 - 45 (1994)
Go to Editor View