Publications

Lee, S.; Rose, S.; Metodiev, M. D.; Becker, L.; Vernaleken, A.; Klopstock, T.; Gailus-Durner, V.; Fuchs, H.; Hrabe De Angelis, M.; Douthwaite, S. et al.; Larsson, N.G.: Overexpression of the mitochondrial methyltransferase TFB1M in the mouse does not impact mitoribosomal methylation status or hearing. Hum Mol Genet 24 (25), pp. 7286 - 94 (2015)

Kukat, C.; Davies, K. M.; Wurm, C. A.; Spahr, H.; Bonekamp, N. A.; Kühl, I.; Joos, F.; Polosa, P. L.; Park, C. B.; Posse, V. et al.; Falkenberg, M.; Jakobs, S.; Kuhlbrandt, W.; Larsson, N.G.: Cross-strand binding of TFAM to a single mtDNA molecule forms the mitochondrial nucleoid. Proc Natl Acad Sci U S A 112 (36), pp. 11288 - 93 (2015)

Lagouge, M.; Mourier, A.; Lee, H.J.; Spahr, H.; Wai , T.; Kukat, C.; Ramos, E.S.; Motori, E.; Busch, J. D.; Siira, S. et al.; Kremmer, E.; Filipovska, A.; Larsson, N.G.: SLIRP Regulates the Rate of Mitochondrial Protein Synthesis and Protects LRPPRC from Degradation. PLoS Genet 11 (8), p. e1005423 (2015)

Milenkovic, D.; Larsson, N.G.: Mic10 Oligomerization Pinches off Mitochondrial Cristae. Cell Metab 21 (5), pp. 660 - 1 (2015)

Bratic, A.; Kauppila, T. E. S.; Macao , B.; Grönke, S.; Siibak, T.; Stewart, J. B.; Baggio, F.; Dols, J.; Partridge, L.; Falkenberg, M. et al.; Wredenberg, A.; Larsson, N.G.: Complementation between polymerase- and exonuclease-deficient mitochondrial DNA polymerase mutants in genomically engineered flies. Nat Commun 6, p. 8808 (2015)

Freyer, C.; Stranneheim, H.; Naess, K.; Mourier, A.; Felser, A.; Maffezzini, C.; Lesko, N.; Bruhn, H.; Engvall, M.; Wibom, R. et al.; Barbaro, M.; Hinze, Y.; Magnusson, M.; Andeer, R.; Zetterstrom, R. H.; von Dobeln, U.; Wredenberg, A.; Wedell, A.: Rescue of primary ubiquinone deficiency due to a novel COQ7 defect using 2,4-dihydroxybensoic acid. J Med Genet 52 (11), pp. 779 - 83 (2015)

Kauppila, J. H. K.; Stewart, J. B.: Mitochondrial DNA: Radically free of free-radical driven mutations. Biochim Biophys Acta 1847 (11), pp. 1354 - 61 (2015)

Mourier, A.; Motori, E.; Brandt, T.; Lagouge, M.; Atanassov, I.; Galinier, A.; Rappl, G.; Brodesser , S.; Hultenby, K.; Dieterich, C. et al.; Larsson, N.G.: Mitofusin 2 is required to maintain mitochondrial coenzyme Q levels. J Cell Biol 208 (4), pp. 429 - 42 (2015)