External Member: Larsson Adjunct Group

Journal Article (201)

2017
Journal Article
Göbel, J.; Motori, E.; Bergami, M.: Spatiotemporal control of mitochondrial network dynamics in astroglial cells. Biochem Biophys Res Commun 500 (1), pp. 17 - 25 (2017)
Journal Article
Brandt, T.; Mourier, A.; Tain, L. S.; Partridge, L.; Larsson, N.G.; Kuhlbrandt, W.: Changes of mitochondrial ultrastructure and function during ageing in mice and Drosophila. Elife 6 (2017)
Journal Article
Milenkovic, D.; Blaza, J. N.; Larsson, N.G.; Hirst, J.: The Enigma of the Respiratory Chain Supercomplex. Cell Metab 25 (4), pp. 765 - 776 (2017)
Journal Article
Siibak, T.; Clemente, P.; Bratic, A.; Bruhn, H.; Kauppila, T. E. S.; Macao, B.; Schober, F. A.; Lesko, N.; Wibom, R.; Naess, K. et al.; Nennesmo, I.; Wedell, A.; Peter, B.; Freyer, C.; Falkenberg, M.; Wredenberg, A.: A multi-systemic mitochondrial disorder due to a dominant p.Y955H disease variant in DNA polymerase gamma. Hum Mol Genet 26 (13), pp. 2515 - 2525 (2017)
2016
Journal Article
Kauppila, J. H. K.; Baines, H. L.; Bratic, A.; Simard, M.-L.; Freyer, C.; Mourier, A.; Stamp, C.; Filograna, R.; Larsson, N.G.; Greaves, L. C. et al.; Stewart, J. B.: A Phenotype-Driven Approach to Generate Mouse Models with Pathogenic mtDNA Mutations Causing Mitochondrial Disease. Cell Rep 16 (11), pp. 2980 - 90 (2016)
Journal Article
Perez-Perez, R.; Lobo-Jarne, T.; Milenkovic, D.; Mourier, A.; Bratic, A.; Garcia-Bartolome, A.; Fernandez-Vizarra, E.; Cadenas, S.; Delmiro, A.; Garcia-Consuegra, I. et al.; Arenas, J.; Martin, M. A.; Larsson, N.G.; Ugalde, C.: COX7A2L Is a Mitochondrial Complex III Binding Protein that Stabilizes the III2+IV Supercomplex without Affecting Respirasome Formation. Cell Rep 16 (9), pp. 2387 - 98 (2016)
Journal Article
Kühl, I.; Miranda, M.; Posse, V.; Milenkovic, D.; Mourier, A.; Siira, S. J.; Bonekamp, N.; Neumann, U.; Filipovska, A.; Polosa, P. L. et al.; Gustafsson, C. M.; Larsson, N.G.: POLRMT regulates the switch between replication primer formation and gene expression of mammalian mtDNA. Sci Adv 2 (8), p. e1600963 (2016)
Journal Article
Rackham, O.; Busch, J. D.; Matic, S.; Siira, S. J.; Kuznetsova, I.; Atanassov, I.; Ermer, J. A.; Shearwood, A. M.; Richman, T. R.; Stewart, J. B. et al.; Mourier, A.; Milenkovic, D.; Larsson, N.G.; Filipovska, A.: Hierarchical RNA Processing Is Required for Mitochondrial Ribosome Assembly. Cell Rep 16 (7), pp. 1874 - 90 (2016)
Journal Article
Richman, T. R.; Spahr, H.; Ermer, J. A.; Davies, S. M.; Viola, H. M.; Bates, K. A.; Papadimitriou, J.; Hool, L. C.; Rodger, J.; Larsson, N.G. et al.; Rackham, O.; Filipovska, A.: Loss of the RNA-binding protein TACO1 causes late-onset mitochondrial dysfunction in mice. Nat Commun 7, p. 11884 (2016)
Journal Article
Ramos, E.S.; Larsson, N.G.; Mourier, A.: Bioenergetic roles of mitochondrial fusion. Biochim Biophys Acta 1857 (8), pp. 1277 - 83 (2016)
Journal Article
Gustafsson, C. M.; Falkenberg, M.; Larsson, N.G.: Maintenance and Expression of Mammalian Mitochondrial DNA. Annu Rev Biochem 85, pp. 133 - 60 (2016)
Journal Article
Bratic, A.; Clemente, P.; Calvo-Garrido , J.; Maffezzini, C.; Felser, A.; Wibom, R.; Wedell, A.; Freyer, C.; Wredenberg, A.: Mitochondrial Polyadenylation Is a One-Step Process Required for mRNA Integrity and tRNA Maturation. PLoS Genetics 12 (5), p. e1006028 (2016)
Journal Article
Gustafsson, C. M.; Falkenberg, M.; Larsson, N.G.: Maintenance and Expression of Mammalian Mitochondrial DNA. Annual review of biochemistry 85, pp. 133 - 160 (2016)
Journal Article
Kauppila, J. H. K.; Baines, H. L.; Bratic, A.; Simard, M.-L.; Freyer, C.; Mourier, A.; Stamp, C.; Filograna, R.; Larsson, N.G.; Greaves, L. C. et al.; Stewart, J. B.: A Phenotype-Driven Approach to Generate Mouse Models with Pathogenic mtDNA Mutations Causing Mitochondrial Disease. Cell reports 16 (11), pp. 2980 - 2990 (2016)
Journal Article
Kühl, I.; Miranda, M.; Posse, V.; Milenkovic, D.; Mourier, A.; Siira, S. J.; Bonekamp, N. A.; Neumann, U.; Filipovska, A.; Polosa, P. L. et al.; Gustafsson, C. M.; Larsson, N.G.: POLRMT regulates the switch between replication primer formation and gene expression of mammalian mtDNA. Science advances 2 (8), p. e1600963 (2016)
Journal Article
Rackham, O.; Busch, J. D.; Matic, S.; Siira, S. .; Kuznetsova, I.; Atanassov, I.; Ermer, J. .; Shearwood, A.-M. J.; Richman, T. .; Stewart, J. B. et al.; Mourier, A.; Milenkovic, D.; Larsson, N.G.; Filipovska, A.: Hierarchical RNA Processing Is Required for Mitochondrial Ribosome Assembly. Cell Reports 16 (7), pp. 1874 - 1890 (2016)
Journal Article
Richman, T. R.; Spåhr, H.; Ermer, J. A.; Davies, S. M. K.; Viola, H. M.; Bates, K. A.; Papadimitriou, J.; Hool, L. C.; Rodger, J.; Larsson, N.G. et al.; Rackham, O.; Filipovska, A.: Loss of the RNA-binding protein TACO1 causes late-onset mitochondrial dysfunction in mice. Nature communications 7, p. 11884 (2016)
Journal Article
Spåhr, H.; Rozanska, A.; Li, X.; Atanassov, I.; Lightowlers, R. N.; Chrzanowska-Lightowlers, Z. M. A.; Rackham, O.; Larsson, N.G.: SLIRP stabilizes LRPPRC via an RRM-PPR protein interface. Nucleic acids research 44 (14), pp. 6868 - 6882 (2016)
Journal Article
Uhler, J. P.; Thörn, C.; Nicholls, T. J.; Matic, S.; Milenkovic, D.; Gustafsson, C. M.; Falkenberg, M.: MGME1 processes flaps into ligatable nicks in concert with DNA polymerase γ during mtDNA replication. Nucleic acids research 44 (12), pp. 5861 - 5871 (2016)
2015
Journal Article
Lee, S.; Rose, S.; Metodiev, M. D.; Becker, L.; Vernaleken, A.; Klopstock, T.; Gailus-Durner, V.; Fuchs, H.; Hrabe De Angelis, M.; Douthwaite, S. et al.; Larsson, N.G.: Overexpression of the mitochondrial methyltransferase TFB1M in the mouse does not impact mitoribosomal methylation status or hearing. Hum Mol Genet 24 (25), pp. 7286 - 94 (2015)
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